Primary Synovial Sarcoma Presenting as a Huge Mass: A Report of a Rare Case and Review of Literature

Document Type : CASE REPORT

Authors

1 Lung Diseases Research Center, Mashhad University of Medical Sciences, Mashhad, Iran

2 Mashhad University of Medical Sciences, Mashhad, Iran

3 Department of Anesthesia, Faculty of Medicine, Mashhad University of Medical Sciences,Mashhad,Iran

4 Endoscopic and Minimally Invasive Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran

5 University of Pennsylvania, Philadelphia, PA, USA

Abstract

Primary synovial sarcoma of mediastinum is very rare among soft tissue sarcomas. Only a few cases have been reported
in the literatures. The best treatment is still unclear, but, surgical resection is the main therapy. In this article we report
a case of a 20*20 cm (2000gr) primary giant mediastinal synovial sarcoma in a 42 year-old man. We performed radical
excision of the tumor and the metastasis.
Level of evidence: V

Keywords


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